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Original Article

A Profile of Glucose-6-Phosphate Dehydrogenase Variants and Deficiency of Multicultural Families in Korea

The Korean Journal of Parasitology 2021;59(5):447-455.
Published online: October 31, 2021

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*Corresponding authors (jangwr@inha.ac.kr; tongsookim@inha.ac.kr)
• Received: July 20, 2021   • Revised: August 11, 2021   • Accepted: August 11, 2021

© 2021, Korean Society for Parasitology and Tropical Medicine

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (https://creativecommons.org/licenses/by-nc/4.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

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A Profile of Glucose-6-Phosphate Dehydrogenase Variants and Deficiency of Multicultural Families in Korea
Korean J Parasitol. 2021;59(5):447-455.   Published online October 22, 2021
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A Profile of Glucose-6-Phosphate Dehydrogenase Variants and Deficiency of Multicultural Families in Korea
Korean J Parasitol. 2021;59(5):447-455.   Published online October 22, 2021
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A Profile of Glucose-6-Phosphate Dehydrogenase Variants and Deficiency of Multicultural Families in Korea
Image
Fig. 1 Distribution of G6PD enzyme activity and genetic variants in the participants in this study. (A) G6PD enzyme activity values for all marriage immigrant women tested in this study; blue bars: participants with normal range G6PD enzyme activity values, red bars: deficient individuals, and green bar: deficient individuals in enzyme activity, but not genotype. (B) G6PD enzyme activity values for all adolescent population tested. (C) G6PD enzyme activity values for male adolescent population tested; blue bars: individuals with normal enzyme activity values, red bars: deficient individuals in enzyme activity and genotype, and green bars: deficient individuals in enzyme activity, but not genotype. (D) G6PD enzyme activity values for female adolescent population tested; blue bars: individuals with normal enzyme activity values, red bars: deficient individuals in enzyme activity and genotype, and purple bars: deficient individuals in genotype, but not enzyme activity.
A Profile of Glucose-6-Phosphate Dehydrogenase Variants and Deficiency of Multicultural Families in Korea

Participants in this study including materfamilias (marriage immigrant women) population and adolescent population

Province County Adolescents Materfamilias Total

Viet. Phil. Camb. Thai. Laos Kazakh. Uzbek. Indon. Russia China
Gangwon Goseong 42 15 12 0 1 0 0 0 0 0 0 28
Yangyang 40 18 9 1 0 0 0 0 0 0 0 28
Donghae 28 23 6 2 2 2 0 0 0 0 0 35
Taebaek 21 8 0 2 0 1 1 1 0 0 0 13
Subtotal 131 64 27 5 3 3 1 1 0 0 0 104

Jeonnam Hwasun 68 26 5 19 0 0 0 0 0 0 0 50
Haenam 16 22 4 6 0 0 0 2 0 1 1 36
Boseong 93 31 12 0 3 0 0 0 1 0 0 47
Hampyeong 69 15 15 13 0 0 0 0 2 0 0 45
Subtotal 246 94 36 38 3 0 0 2 3 1 1 178

Gyeonggi Yeoncheon 40 28 3 0 0 0 0 0 0 0 3 34
Subtotal 40 28 3 0 0 0 0 0 0 0 3 34

Total 417 186 66 43 6 3 1 3 3 1 4 316

Viet.: Vietnam, Phil.: Philippines, Camb.: Cambodia, Thai.: Thailand, Kazakh.: Kazakhstan, Uzbek.: Uzbekistan, Indon.: Indonesia.

Demographic characteristics of participants surveyed

Characteristics Materfamilias (n=316) Adolescents (Male) (n=219) Adolescents (Female) (n=198) Adolescents (Total) (n=417)
Age (yr), mean±SD 34.9±8.0 8.7±4.1 9.0±4.1 8.8±4.1

Hb count (g/dL), mean±SD 13.2±1.2 13.5±1.1 13.0±1.1 13.2±1.1

Mean G6PD activity (U/g Hb), mean±SD 11.5±2.7 11.6±2.8 12.3±2.0 11.9±2.4

G6PD deficient [n (%)] 10 (3.2%) 17 (7.8%) 4 (2.0%) 21 (5.0%)

Extreme G6PD activity, mean±SD 20.2±3.7 21.6±0.5 19.0±2.4 19.9±2.3

WHO classification of deficiency
Severe (<10%) 1 (0.3%) 11 (5.0%) 11 (2.6%)
Moderate (10% to <30%) 4 (1.3%) 4 (1.8%) 1 (0.5%) 5 (1.2%)
Mild (30% to <60%) 5 (1.6%) 2 (0.9%) 3 (1.5%) 5 (1.2%)
Normal (≥60% to <150%) 295 (93.4%) 200 (91.3%) 190 (96.0%) 390 (93.5%)
Extreme (≥150% or >16.3 U/g Hb) 11 (3.5%) 2 (0.9%) 4 (2.0%) 6 (1.4%)

Distribution of the adolescent population in the multicultural families in this study

Countries Countries of Materfamilias Sub-total

Vietnam Philippines Cambodia Thailand Laos Other Countriesa







Male Female Male Female Male Female Male Female Male Female Male Female Male Female
Goseong 8 15 6 10 0 0 1 2 0 0 0 0 15 27
1b 1 1 1 2

Yangyang 18 9 6 4 1 2 0 0 0 0 0 0 25 15
1 2c 1 2 2

Donghae 8 13 3 0 1 0 2 0 1 0 0 0 15 13
1 1 1 3

Taebaek 7 6 0 0 3 1 0 0 1 0 2 1 13 8
2 2

Hwasun 27 11 1 3 9 17 0 0 0 0 0 0 37 31
1 2 1 2

Haenam 6 2 0 1 3 4 0 0 0 0 0 0 9 7
1 1

Boseong 32 31 9 11 0 0 3 5 0 0 2 0 46 47
1 1

Hampyeong 15 12 12 9 8 9 0 0 0 0 4 0 39 30
4 1 4 1

Yeoncheon 17 15 1 1 0 0 0 0 0 0 2 4 20 20
1 1d 1 1

Total 138 114 38 39 25 33 6 7 2 0 10 5 219 198
4 3 1 1 2 1 5 2 1 1 1 2 12 5 4 3

aOther countries contain Kazakhstan, Uzbekistan, Indonesia, Russia, and China.

bItalic and -colored numbers mean the numbers of deficient individuals in both enzyme-activity and genotype.

c -colored numbers mean the numbers of deficient individuals in enzyme activity, but not in genotype.

d -colored numbers mean the numbers of deficient individuals in genotype, but not in enzyme-activity.

Distribution of the foreign immigrant woman population in the multicultural families in this study

Collection Sites Countries of Materfamilias Total

Vietnam Philippines Cambodia Thailand Laos Other Countriesa
Goseong 15b 12 1 28
1c 1d 1 1

Yangyang 18 9 1 28
1 1 2

Donghae 23 6 2 2 2 35
1 1 1 1 1 3

Taebaek 8 2 1 2 13
1 1

Hwasun 26 5 19 50
1 1e 2 1 2 1

Haenam 22 4 6 4 36
1 1 1 1 2

Boseong 31 12 3 1 47
1 1 2

Hampyeong 15 15 13 2 45
1 1 3 2 3

Yeoncheon 28 3 3 34
2 2

Total 186 66 43 6 3 12 316
4 2 1 2 4 2 6 2 1 1 8 15 2

aOther countries contain Kazakhstan, Uzbekistan, Indonesia, Russia, and China.

bTotal number of the foreign immigrant women which were tested for the G6PD activity.

c -colored numbers mean the numbers of deficient individuals in both enzyme-activity and genotype.

d -colored numbers mean the numbers of deficient individuals in genotype, but not enzyme-activity (Normal range).

e -colored numbers mean the numbers of deficient individuals in enzyme activity, but not genotype.

Correlation of phenotype with genotype by gender in male adolescent population and materfamilias population

Participants Phenotype No. of participants Genotype No. of participants (%) Enzyme activity (U/g Hb)

Mean±SD Range
Male adolescents (n=219) Normal 202 Wild-type 202 (92.2) 12.1±1.8 8.5–22.5
Hemizygous 0 (0)
Deficient 17 Wild-type 5 (2.3) 4.2±1.2 3.2–6.4
Hemizygous 12 (5.5) 0.6±0.4 <0.5–1.7

Female adolescents (n=198) Normal 194 Wild-type 192 (97.0) 12.4±1.8 8.9–22.1
Heterozygous 3 (1.5) 10.9±0.5 10.5–11.7
Homozygous 0
Deficient 4 Wild-type 0
Heterozygous 4 (2.0) 5.5±1.1 3.8–6.5
Homozygous 0

Materfamilias (n=316) Normal 306 Wild-type 291 (92.1) 11.8±2.5 8.1–20.5
Heterozygous 15 (4.7) 9.7±1.1 8–12.1
Homozygous 0
Deficient 10 Wild-type 2 (0.6) 6.2 6.1–6.2
Heterozygous 7 (2.2) 4.2±1.8 2.6–6.2
Compound 1 (0.3) <0.5 <0.5
Heterozygous

Total 733 733
Table 1 Participants in this study including materfamilias (marriage immigrant women) population and adolescent population

Viet.: Vietnam, Phil.: Philippines, Camb.: Cambodia, Thai.: Thailand, Kazakh.: Kazakhstan, Uzbek.: Uzbekistan, Indon.: Indonesia.

Table 2 Demographic characteristics of participants surveyed
Table 3 Distribution of the adolescent population in the multicultural families in this study

Other countries contain Kazakhstan, Uzbekistan, Indonesia, Russia, and China.

Italic and -colored numbers mean the numbers of deficient individuals in both enzyme-activity and genotype.

-colored numbers mean the numbers of deficient individuals in enzyme activity, but not in genotype.

-colored numbers mean the numbers of deficient individuals in genotype, but not in enzyme-activity.

Table 4 Distribution of the foreign immigrant woman population in the multicultural families in this study

Other countries contain Kazakhstan, Uzbekistan, Indonesia, Russia, and China.

Total number of the foreign immigrant women which were tested for the G6PD activity.

-colored numbers mean the numbers of deficient individuals in both enzyme-activity and genotype.

-colored numbers mean the numbers of deficient individuals in genotype, but not enzyme-activity (Normal range).

-colored numbers mean the numbers of deficient individuals in enzyme activity, but not genotype.

Table 5 Correlation of phenotype with genotype by gender in male adolescent population and materfamilias population